Background
VHL gene abnormality — 1 / 36,000 individuals Renal cell carcinomas and pancreatic NETs are true cancers and can result in mets and death
•Pancreas is involved in 15% of patient with VHL
•Major pancreatic surgery for VHL is recommended if
-symptomatic large (>5 cm) serous cystadenomas or
-neuroendocrine pancreatic tumor (pNENs) > 2 cm appear
